Renal primitive neuroectodermal tumour in childhood: Case report and review of literature

Authors

  • Maeed Asiri Department of Urology, King Abdul Aziz University Hospital, Jeddah, Kingdom of Saudi Arabia
  • Ahmed Al-Sayyad Department of Urology, King Abdul Aziz University Hospital, Jeddah, Kingdom of Saudi Arabia

DOI:

https://doi.org/10.5489/cuaj.969

Abstract

Primitive neuroectodermal tumour (PNET) is presumed to be of
neural crest origin, mostly presenting as bone or soft tissue masses.
It usually occurs in the trunk or axial skeleton; while renal PNET is
considered an extremely rare tumour. We report a case of 11-yearold
male who presented with right flank pain and gross hematuria
after suffering blunt trauma. During investigations, he was found to
have a large renal mass on computed tomography. He underwent
a right radical nephrectomy where the pathology report showed
PNET of the kidney. The patient received chemotherapy afterwards.
Despite the chemotherapy, he had a local tumour recurrence 3
months after and continued to deteriorate and developed distant
metastasis. Primitive neuroectodermal tumour of the kidney is a
distinct and rare entity. It is very aggressive, with a poor survival
despite combined modality treatment.

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Author Biographies

Maeed Asiri, Department of Urology, King Abdul Aziz University Hospital, Jeddah, Kingdom of Saudi Arabia

Ahmed Al-Sayyad, Department of Urology, King Abdul Aziz University Hospital, Jeddah, Kingdom of Saudi Arabia

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How to Cite

Asiri, M., & Al-Sayyad, A. (2013). Renal primitive neuroectodermal tumour in childhood: Case report and review of literature. Canadian Urological Association Journal, 4(6), E158-E160. https://doi.org/10.5489/cuaj.969

Issue

Section

Case Report